The patient was a 24-year-old Korean man with an extensive nevus flammeus over the right buttock, penis, leg, ankle and dorsal aspect of foot. Varicose veins on the flexor aspect of mid-portion of lower extremity of right side are noted remarkable hypertrophy of the soft tissue and bones are also found on the area where hemangioma is associated with them. Radiological examination of spine, pelvic, femur, tibia and fibula bones showed longer and thicker in affected side (right) than unaffected. (left), and vertebral bones showed compensatory scoliosis-convexity to the left (normal side)-and damage of vertebral bodies at the level of L-3,4,5.
These are well established and described as Klippel-Trenaunay-Parkes Weber Syndrome by Klippel, Trenaunay and Parkes-Weber. Authors are made extensive review of literatures of the syndrome and discussions on the type, varient, heredity, sex, onset of age, affected location, racial distribution, right name of syndrome and differential diagnosis of the syndrome.
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